以红皮症表现的皮肌炎-dermatol.PDFVIP

以紅皮症表現的皮肌炎 -病例報告 陳嘉偉1 蔡呈芳2 陳佑甫1 洪志明1 秀傳紀念醫院皮膚科1 國立台灣大學醫學院附設醫院皮膚科2 Dermatomyositis Presenting with Erythroderma -A Case Report Chia-Wei Chen1 Tsen-Fang Tsai2 Yu-Fu Chen1 Chih-Ming Hung1 Dermatomyositis is a common autoimmune disorder characterized by both cutaneous and muscle involvement. The characteristic cutaneous features included photosensitivity and the presence of heliotrope erythema and Gottrons papules. A number of uncommon cutaneous manifestations had been reported. We reported a female patient who developed erythroderma after dermatomyositis was diag- nosed ten years later. (Dermatol Sinica 25: 200-204, 2007) Key words: Dermatomyositis, Erythroderma, Occult malignancy 皮肌炎是一種以皮膚和肌肉侵犯表現的自體免疫性疾病。當中最具特色的皮膚表現包括 光敏感性禿heliotrope erythema 禿和Gottron’s papules 。有許多不常見的皮膚表現曾緩被報告 過。這次我們報告一位女性病人在診斷皮肌炎十年後出現紅皮症。(中華皮誌25: 200-204, 2007) From the Department of Dermatology, Show Chwan Memorial Hospital1 and National Taiwan University Hospital2 Accepted for publication: January 29, 2007 Reprint requests: Chih-Ming Hung, M.D., Department of Dermatology, Show Chwan Memorial Hospital, 542, Sec.1 Chung-Shang Rd. Changhua, Taiwan, R.O.C. TEL: 886-4-7256166 ext. 81210 FAX: 886-4-7236226 Dermatol Sinica, Sep 2007 200 陳嘉偉 INTRODUCTION In August 2005, she visited the rheumato- In 1863, Wagner first recognized dermato- logic clinic in our hospital. Abnormal laborato- myositis/polymyositis. In 1891, Unverricht pro- ry values included total IgE2000 KU/L(250), vided the first description of dermatomyositis. Hb 9.1 gm/dl(12-16), Eosinophil 28%(0.0-4.0), Dermatomyosi