VONHIPPELLINDAUDISEASE-Neuroradiology.pptVIP

VONHIPPEL LINDAU DISEASE Rheumatoid arthritis Viral myelitis * Complex cystic lesion in the conus medullaris region with enhancing mural nodules. Enhancing focus along thoracic cord Intramedullary enhancing nodule in lower thoracic cord. History: 12 year-old female with history of von Hippel Lindau disease. Diagnosis: von Hippel Lindau Disease with spinal hemangioblastomas. ACR Code: 38.3651 -- About 20% of spinal hemangioblastoma cases are associated with von Hippel-Lindau disease -- Hemangioblastoma accounts for about 1-15% of all cord tumors, in which 85-90% are intramedullary. -- MRI