畸形：无、巨脑畸形.docVIP

F/0.5Y。患儿主要表现为癫痫，近一个月来频发。五官尚可，头颅大小与同龄儿相比稍小，智力低下（平时家人斗小孩时目光及动做迟缓）。 结果： 无脑回畸形伴胼胝体发育不良 男，8个月，间歇性惊厥3个月。患儿体检无明显异常发现，心肺正常。血常规正常。今日临床以脑炎？要求CT检查。平扫显示大脑半球皮质明显增厚，脑白质减少，两侧额顶脑沟少而浅，呈现巨大脑回表现，部分大脑皮质缺乏沟回，：巨脑回畸形。女性，22岁，左侧上下肢瘫痪21年结果：巨脑回畸形 [病理]??????无脑回畸形和/或巨脑回畸形：?无脑回畸形指大脑表面光滑，无脑回结构；巨脑回畸形指大脑停留在原始阶段，脑回宽、扁。两者仅为畸形成度不同，可同时存在于脑的不同部位。前者多在顶枕部，后者多位于额部。镜下管前者大脑皮质结构异常，皮质分层不完全或不分层，常见不成熟的神经细胞。后者皮层保留了原始皮层的4曾神经细胞结构，神经细胞分化不成熟。白质中常发现异位的神经细胞，有时呈结节状。[临床表现]??????无脑回畸形患儿在新生儿期常有小头畸形和轻微面部异常，以后表现出智力落后。完全性无脑回畸形者大多在2岁前死亡。巨脑回存活者常有智力低下和癫痫。[CT表现]??????无脑回畸形和/或巨脑回畸形，前者主要表现为脑表面光滑，脑回、脑沟消失，皮层增厚，白质减少。后者主要表现为侧裂变浅、增宽，脑回增宽，皮质增后，内表面光滑，白质减少，患侧脑室系统扩大。此外，无脑回畸形两侧裂变浅，呈“8”字形表现。 [本例CT平扫]??????显示双侧大脑半球皮层明显增厚、表面光滑、无脑回及脑沟，皮层下白质稀少。双侧外侧裂变浅、凹陷，整个双侧大脑半球呈“8”字形表现，脑室系统扩大。前纵裂增宽、增深，与第三脑室向连通。双侧侧脑室扩大、分离。????? the Communist Party of China, and a deep understanding of the partys nature, purpose, guiding principles, goals, organization, good style, deeply understand the conditions, rights and obligations of members, code of conduct, bearing in mind that oath, clear Members of the standards and conditions, enhance respect, abide by the Constitution, maintaining the party Constitution consciousness of the party Constitution. Read through the familiar with the code of self-discipline of the CPC, the CPC disciplinary regulations, members of the Communist Party of China party regulations on rights protection Ordinance, mastering self-discipline standards of four must, the four upholdings, mastering various types of disciplinary offence and punishment provisions and clear what you can do, what they cant do. 2. speech understanding learning series XI series the basic spirit of an important speech by General Secretary, learn to understand the Party Central Committee on governance of the new concept of basic elements of new ideas and new strategies, master and strengthen the party spirit, fulfills the purpose ideas, moral character, conservation related to the basic requirements. Learning of the XI series read the im