Peutz-Jeghers syndrome caused by multiple one cases of intussusception and intestinal necrosis.doc

 PAGE \* MERGEFORMAT 5 Peutz-Jeghers syndrome caused by multiple one cases of intussusception and intestinal necrosis [Keywords:] Peutz-Jeghers syndrome, intussusception, intestinal necrosis Peutz-Jeghers syndrome (Peutz  Jeghers syndrome, PJS) is a autosomal dominant genetic disease, clinically very rare in recent years. More a result of gastrointestinal bleeding, abdominal pain, or even intestinal obstruction and treatment, I admitted to a hospital with Multiple intussusception and intestinal necrosis in patients are reported as follows. Patients, male, 28 years old. 48 h had no significant incentive to appear before the abdominal cramps, mainly in order to Cullen and lower abdominal pain was paroxysmal, non-diffuse, with nausea, no vomiting, no fever, chest pain and cough, symptomatic treatment in community hospitals, the effect poor. Symptoms gradually worsened and stop the exhaust, defecation, so come to my hospital emergency room. Patients customarily weaker constitution, there had been abdominal pain, abdominal distention and similar attacks, but mild symptoms, diagnosis and treatment were not their own ease. Become ill due to poor diet, sleep is acceptable to urinate less color depth. Admission examination: body temperature 37.6 ℃ , pulse 110 times / min, breathing 19 times / min, blood pressure 120/60 mmHg (1 mmHg = 0  133 kPa). Lips, oral mucosa, hands and feet can be seen scattered melanin spot, no swelling of superficial lymph nodes, heart and lung checkup found no abnormalities. Abdomen: The belly bulge, especially in the lower abdomen for the drama, abdominal breathing is not restricted, no significant intestinal shape and peristaltic waves, below the belly button to the lower abdomen can reach a median of about 10 cm * 20 cm size, mass, tenderness, rebound tenderness (± ), marked muscular tension. Percussion drum sound, shifting dullness negative shock the water sound negative, bowel sounds disappear. Routine blood test: WBC 15.3 * 109 / L,