2018IAP共识声明:血友病的诊断和管理.pdfVIP

2018IAP共识声明:血友病的诊断和管理.pdf

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RR EE CC OO MM MM EE NN DD AA TT II OO NN SS R E C O M M E N D A T I O N S RR EE CC OO MM MM EE NN DD AA TT II OO NN SS Consensus Statement of the Indian Academy of Pediatrics in Diagnosis and Management of Hemophilia ANUPAM SACHDEVA1, VINOD GUNASEKARAN1, HN RAMYA1, JASMITA DASS1, JYOTI KOTWAL1, TULIKA SETH2, SATYARANJAN DAS3, KAPIL GARG4, MANAS KALRA5, SIRISHA RANI S6 AND ANAND PRAKASH7; FOR THE ‘CONSENSUS IN DIAGNOSIS AND MANAGEMENT OF HEMOPHILIA’ COMMITTEE*, INDIAN ACADEMY OF PEDIATRICS. 1 2 3 5 From Sir Ganga Ram Hospital, All India Institute of Medical Sciences, Army Hospital Research and Referral, Indraprastha Apollo Hospitals, New Delhi; 4Sawai Man Singh Medical College, Jaipur; 6Rainbow Children’s Hospital, Hyderabad; 7St Johns Medical College Hospital, Bangalore; India. *As per Annexure on last page. Correspondence: Dr Anupam Sachdeva, Director, Pediatric Hematology Oncology and Bone Marrow Transplantation unit, Institute for Child Health, Sir Ganga Ram Hospital, New Delhi 110 060, India. anupamace@yahoo.co.in Justification: Despite having standard principles of management of hemophilia, treatment differs in various countries depending on available resources. Guideline for management of hemophilia in Indian setting is essential. Process: Indian Academy of Pediatrics conducted a consultative meeting on Hemophilia on 18th September, 2016 in New Delhi, which was attended by experts in the field working across India. Scientific literature was reviewed, and guidelines were drafted. All expert committee members reviewed the final manuscript. Objective: To bring out consensus guidelines in diagnosis and management of Hemophilia in India. Recommendations: Specific factor assays confir

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