Ebstein畸形的外科治疗.ppt

Ebstein畸形的外科治疗策略 Ebstein畸形是罕见复杂的心脏先天畸形 发生率1:40,000-200,000 先天性心脏病中: 1% 疾病谱宽： 轻型 无症状 重症 新生儿期死亡率极高 手术死亡率高 解剖学特点 Displacement of the septal and posterior leaflets of the TV toward the apex of the RV. Although the anterior leaflet is attached at the appropriate level of the tricuspid annulus, it is larger than normal and may have multiple chordal attachments to the ventricular wall. 3. The segment of the RV from the level of the true tricuspid annulus to the level of attachment of the septal and poster