distinct roles for laminin globular domains in laminin α1 chain mediated rescue of murine laminin α2 chain deficiency不同的角色在层粘连蛋白层粘连蛋白的球状域α1链介导拯救鼠层粘连蛋白α2链不足.pdfVIP
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distinct roles for laminin globular domains in laminin α1 chain mediated rescue of murine laminin α2 chain deficiency不同的角色在层粘连蛋白层粘连蛋白的球状域α1链介导拯救鼠层粘连蛋白α2链不足
Distinct Roles for Laminin Globular Domains in Laminin
a1 Chain Mediated Rescue of Murine Laminin a2 Chain
Deficiency
¤
˚
Kinga I. Gawlik, Mikael Akerlund, Virginie Carmignac, Harri Elamaa , Madeleine Durbeej*
Department of Experimental Medical Science, Muscle Biology Unit, University of Lund, Lund, Sweden
Abstract
Background: Laminin a2 chain mutations cause congenital muscular dystrophy with dysmyelination neuropathy (MDC1A).
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