BSR amp; BHPR Guidelines for the Management of adults with ANCA BSR amp；BHPR指引ANCA成人的管理.docxVIP

BSR Guidelines for the Management of adults with ANCA Associated VasculitisChair of the Guideline Working Group: Dr Richard A WattsApril 2013Section 1 Scope and Purpose1.1 Background to VasculitisThe primary systemic vasculitides are heterogeneous, multi-system disorders characterised by inflammation and necrosis of small and medium blood vessels. Their aetiology is unknown. Three distinct clinico-pathological syndromes, often associated with anti-neutrophil cytoplasmic antibodies (ANCA), called ANCA associated vasculitis (AAV), have been identified and collectively comprise the most common su