《杨仁池 血友病防治的进展》ppt课件.pptVIP

血友病防治的进展;概况; 血友病的严重程度与出血;国内现状;WFH Global Survey 2001/2;WFH Global Survey 2004;WFH Global Survey 2004;;;Current Data;Hemophilia and related disorders in Tianjin Hemophilia Center (1980-2002.6);Arthropathy in different ages;;;;AIDS in recipient of coagulation factor concentrates (1978-85);;;;;;;血友病的基因治疗; 血友病出血的治疗原则;血友病的出血部位 ;替代治疗指南 出血类型 FVIII剂量（U/kg） FIX剂量（U/kg） 因子水平(%) 急性关节出血 10-20，q.12h 15, q.24 30-50 肌肉内 20-30, q12h 40-60, q.24h 40-50 CNS 50, q12h, 或连续输注 100，然后50, q24h 开始100，然后 50-100，10-14d 损伤或外科 50, q12h, 或连续输注 100, q24h 100, 然后50, 至伤口开始愈合， 然后30至痊愈 咽后壁 50, q12h, 4d 40, q24h, 4d 50-70 胃肠道 50, q12h, 3d, 40, q24h, 3d 50-100 或直至出??减轻 或直至出血减轻 血尿 40，3-5d 40, 3d 50 拔牙 20,一次，EACA 40,一次，EACA 50 100mg/kg, 7-10d 100mg/kg, 7-10d 腹膜后 50, q12h, 6d 100, q24h, 6d 开始100，然后 50，直至痊愈 ;China A Prioritized Project, WFH;China A Prioritized Project, WFH;1993 – 1997: Education and Training;1997 – 2001/02: Hemophilia Twinning Centres and Treatment Centre Development;Patient Group Activities / Leadership;Vision for a National Strategy;At the Regional Hemophilia Care Conference, Guangzhou, Nov 2001, the professional groups agreed on: (1) Three priority projects for urgent development: (i) A National Registry (ii) Hemophilia Nursing (iii) Coagulation testing workshops. (2) A strategy to formulate a National Body, later formalized as the “Hemophilia Treatment Centre Collaborative Network, China”.;Project Progress;2002 – 2004: A Country Program with a Hemophilia Treatment Centre Network, China; WFH Hemophilia Conference  March 2004, Jinan, China ;A NETWORK OF HEMOPHILIA TREATMENT CENTRES HAS BEEN ESTABLISHED AS A SOLID FOUNDATION TO PROMOTE HEMOPHILIA CARE IN CHINA FOR THE FUTURE.;Challenges Ahead;现状;Publication;Acknowledgement