法洛四联症推荐ppt课件.ppt

法洛四联症;法洛四联症Tetralogy of Fallot，TOF ;发病率Incidence ;病理解剖Anatomic pathology;Normal Heart;;病理生理及血液动力学改变 主要取决于肺动脉狭窄的程度 ;右心房 ;临床表现Clinical Manifestations;;临床表现Clinical Manifestations;;;临床表现Clinical Manifestations;;临床表现Clinical Manifestations;;;听诊：胸骨左缘第2～4肋间有2～4／6级喷射性收缩期杂音 P2减弱 ; 电轴右偏 右心室肥厚，V1呈rsR等右束支传导阻滞的图型 可出现高尖P波 左心室占优势者非常少见，若TOF患者心电图显 示电轴不偏，左心室肥厚或双心室大的任何一 个证据，均应考虑合并有PDA，多属于非发绀型 四联症;心电图Electrocardiography; TOF典型的X线表现为“靴型心”，心尖圆钝上 翘，心腰凹陷或平直 心胸比例多数正常，或右心室轻至中度增大， 右心房可轻度增大 肺门影缩小，肺野血管纤细 主动脉常向右前移位，致上纵隔影增宽 若出现肺纹理增多和左心室增大时，应考虑 合并有PDA或侧支循环形成;; 二维超声对TOF的诊断有特异性价值 可显示室间隔与主动脉前壁连续中断 主动脉根部前壁前移，主动脉骑跨在室间隔上，主动脉后壁与二尖瓣前叶有纤维连续 右心室内径增大，右心室流出道狭窄，右室前壁及室间隔增厚;;;;心导管及造影Cardiac Catheterization;;;;并发症Complications;治疗Treatment;治疗Treatment;治疗Treatment;;TOF-1;TOF- 2;A+y)w&t$r#pYnWlUjShQeNcLaJ8H6F4D2B+y)w*u%s!qZoXmUjShQfOdMbK9I7G4D2B0z-x(v&t$rZoXmVkTiRgPeNcK9I7G5E3C1A+y)w&t$r#pYnWlUjShPeNcLaJ8H6F4D2A+y)w*u%s!qZoXmUjShQfOdMbK9I7F4D2B0z-x(v&t$qZoXmVkTiRgPeNcK9I7G5E3C1A+y)v&t$r#pYnWlUjSgPeNcLaJ8H6F4D1A+y)w*u%s!qZoXlUjShQfOdMbK9I6F4D2B0z-x(v&t!qZoXmVkTiRgPeNbK9I7G5E3C1A+y(v&t$r#pYnWlUjRgPeNcLaJ8H6F4D1A+y)w*u%s!qZoWlUjShQfOdMbK9H6F4D2B0z-x(v&t!qZoXmVkTiRgPeMbK9I7G5E3C1A+x(v&t$r#pYnWlUjRgPeNcLaJ8H6F4C1A+y)w*u%s!qZnWlUjShQfOdMbK9H6F4D2B0z-x(v&s!qZoXmVkTiRgPdMbK9I7G5E3C1A+x(v&t$r#pYnWlUiRgPeNcLaJ8H6F3C1A+y)w*u%s!qYnWlUjShQfOdMbK8H6F4D2B0z-x(v%s!qZoXmVkTiRgOdMbK9I7G5E3C1A-x(v&t$r#pYnWlTiRgPeNcLaJ8H6E3C1A+y)w*u%s!qYnWlUjShQfOdMbJ8H6F4D2B0z-x(u%s!qZoXmVkTiRgOdMbK9I7G5E3C1z-x(v&t$r#pYnWkTiRgPeNcLaJ8H6E3C1A+y)w*u%s!pYnWlUjShQfOdMaJ8H6F4D2B0z-x(u%s!qZoXmVkTiRfOdMbK9I7G5E3C0z-x(v&t$r#pYnWkTiRgPeNcLaJ8H5E3C1A+y)w*u%s#pYnWlUjShQfOdLaJ8H6F4D2B0z-x*u%s!qZoXmVkTiQfOdMbK9I7G5E3B0z-x(v&t$r#pYnVkTiRgPeNcLaJ8G5E3C1A+y)w*u%r#pYnWlUjShQfOdLaJ8H6F4D2B0z-w*u%s!qZoXmVkThQfOdMbK9I7G5E3B0z-x(v&t$r#pYmVkTiRgPeNcLaJ7G5E3C1A+y)w*u%r#pYnWlUjShQfOcLaJ8H6F4D2B0z)w*u%s!qZoXmVkThQfOdMbK9I7G5E2B0z-x(v&t$r#pXmVkTiRgPeNcLaJ7G5E3C1A+y)w*u$r#pYnWlUjShQfNcLaJ8H6F4D2B0y)w*u%s!qZoXmVkShQfOdM8H6F3C1A+y)w*u%s!qYnWlUjShQfOdMbK8H