先天性巨结肠与胆道剖析.pptxVIP

2020/12/18;定义 Defination;Hirschsprung’s Disease,HD 赫什朋氏病Aganglionosis 先天性无神经节细胞症;概述 Summary ;病 因Etiology;胚胎期第5周消化道神经母细胞从头端向尾端移行 Neuroblastoma?cells of digestive tract migrate?from the beginning to the end In the fifth week of fetal.;;Absence of?ganglion cells ;; 按病变长度According to the length of lesion segment 常见型Ordinary type?(common?type)?megacolon (85%): Lesion is?limited in?rectum and sigmoid colon. 短段型Short?segment type megacolon(10%): Lesion is?limited in the?distal 3-4?cm?of rectum. 长段型Long?segment type megacolon(10%): Lesion reaches splenic flexure,?and even?the entire colon. 全结肠型Tot