门静脉高压症少见成因及诊断.pptxVIP

门静脉高压症少见成因及诊断;定义;门静脉压力值 1kpa =10.2cmH2O;门静脉解剖特点;;第6页/共50页;解剖概要：;病因;门静脉高压形成后的病理生理变化; 胰源性门脉高压症 (pancreatic portal hypertension, PPH);胰源性门脉高压;胰源性门脉高压发生率;门脉小循环 (脾胃血流区);PPH形成机制;PPH临床特点;PPH诊断;PPH诊断;门静脉血栓形成(portal vein thrombosis, PVT);门静脉血栓形成;门静脉海绵样变性(cavernous transformation of the portal vein, CTPV）;门静脉海绵样变性诊断;门静脉海绵样变性;23;24;25;26;BCS的诊断依据;Budd-Chiari综合征;右心衰竭 ;心包缩窄;肝窦阻塞综合征(hepatic sinusoidal obstruction syndrome, SOS);32;33;血色病(hemochromatosis, HC);肝血色病的发生原因;肝血色病;肝淀粉样变(hepatic amyloidosis);骨髓增生性疾病(myeloproliferative disease, MLD);骨髓增生性疾病诊断依据;先天性肝纤维化(congenital hepatic fibr