ANCA相关小血管炎的诊治策略和研究进展要点.ppt

426 patients,：Wegener’s granulomatosis，87 (20.4%) Microscopic polyangiitis，337 (79.1%) Churg-Strauss syndrome，2 (0.5%) All patients had multisystem involvement. kidney involvement，371 (87.1%) lung involvement，260 (61.0%) Renal involvement ： MPO-p-ANCAPR3-c-ANCA The one（ 13.1% ）and five year （22.4%）death rates The end stage renal disease at one（15.9%）and five years（27.1%） Conclusions: AAV is not a rare autoimmune disease in Chinese people. Kidney and lung were the most vul