Concomitant Aortoplasty with Septal Myectomy for Supravalvar Aortic Stenosis in an Adult英文文献资料.docVIP

World Journal of Cardiovascular Surgery, 2012, 2, 5-6 5 /10.4236/wjcs.2012.21002 Published Online March 2012 (http://www.SciRP.org/journal/wjcs) Concomitant Aortoplasty with Septal Myectomy for Supravalvar Aortic Stenosis in an Adult Raja Saravanan Elumalai , Kirthivasan Vaidyanathan , Madhu Sankar Nainar , 1* 1 2 2 2 3 Karthik Vaidyanathan , Govini Balasubramaniam , Susan George 1 Department of Cardiac Anaesthesiology, Global Hospital and Health City, Perumbakkam, India Department of Cardiothoracic Surgery, Global Hospital and Health City, Perumbakkam, India Department of Cardiology, Global Hospital and Health City, Perumbakkam, India 2 3 Email: drrajasaravanan@ * Received December 3, 2011; revised January 13, 2012; accepted February 13, 2012 ABSTRACT Survival of patients with severe congenital aortic stenosis beyond third decade is uncommon. This report describes a 31 year old patient who underwent successful aortoplasty and in addition septal myectomy for complete relief of left ven- tricular outflow obstruction. Keywords: Aortoplasty; Myectomy; Supravalvar Aortic Stenosis 1. Introduction Congenital Supravalvar Aortic Stenosis is a rare form of obstructive lesion of the left ventricular outflow tract. The defining feature of the malformation is an aortic narrowing at the level of the sino tubular junction. The commonly associated lesions include peripheral pulmo- nary artery lesions, coronary lesions, abnormalities of the aortic leaflets and diffuse narrowing of ascending aorta. Survival beyond three decades is uncommon and this report describes a case of supravalvar aortic stenosis in a 31 year old patient who underwent successful aortoplasty and septal myectomy. 2. Case S