【2017年整理】骨纤维异常增殖症.ppt

【2017年整理】骨纤维异常增殖症

骨纤维异常增殖症;定义;;;分型;其他分类;可发生于全身任何骨骼,以四肢长管状骨,尤以股骨最多见,其次是肋骨、颅面骨 ;病理改变;临床表现;伴有病理性骨折;X线表现;单骨型及多骨型;;CT表现;;;;Evaluation only. Created with Aspose.Slides for .NET 3.5 Client Profile 5.2.0.0. Copyright 2004-2011 Aspose Pty Ltd.;Evaluation only. Created with Aspose.Slides for .NET 3.5 Client Profile 5.2.0.0. Copyright 2004-2011 Aspose Pty Ltd.;MR表现;;;;;;;;;;;;;患者女,25岁,主因右下肢不适就诊;;;;;Evaluation only. Created with Aspose.Slides for .NET 3.5 Client Profile 5.2.0.0. Copyright 2004-2011 Aspose Pty Ltd.;Evaluation only. Created with Aspose.Slides for .NET 3.5 Client Profile 5.2.0.0. Copyright 2004-2011 Aspose Pty Ltd.;Evaluation only. Created with Aspose.Slides for .NET 3.5 Client Profile 5.2.0.0. Copyright 2004-2011 Aspose Pty Ltd.;患者女性,40岁;Evaluation only. Created with Aspose.Slides for .NET 3.5 Client Profile 5.2.0.0. Copyright 2004-2011 Aspose Pty Ltd.;Evaluation only. Created with Aspose.Slides for .NET 3.5 Client Profile 5.2.0.0. Copyright 2004-2011 Aspose Pty Ltd.;Evaluation only. Created with Aspose.Slides for .NET 3.5 Client Profile 5.2.0.0. Copyright 2004-2011 Aspose Pty Ltd.;Evaluation only. Created with Aspose.Slides for .NET 3.5 Client Profile 5.2.0.0. Copyright 2004-2011 Aspose Pty Ltd.;Evaluation only. Created with Aspose.Slides for .NET 3.5 Client Profile 5.2.0.0. Copyright 2004-2011 Aspose Pty Ltd.;Evaluation only. Created with Aspose.Slides for .NET 3.5 Client Profile 5.2.0.0. Copyright 2004-2011 Aspose Pty Ltd.;鉴别诊断;骨化性纤维瘤是一种少见的原发性良性骨肿瘤,可累及全身骨骼,其中85%累及面骨,以下颌骨多见,长管状骨少见。好发部位为胫腓骨,仅占原发性骨肿瘤的0.7% 影像学与骨纤维异常增殖症表现极易混淆,好发于胫骨骨干中上段的前缘,少数可同时发生于腓骨的中下段。病灶位于骨皮质内,呈溶骨性骨质破坏,密度常不均匀,骨皮质变薄,內缘消失,髓腔变窄,病变部位无疼痛感,但略增粗,常向前轻度弯曲,无软组织肿块。 ;单纯骨囊肿 单纯性骨囊肿呈边缘光整的椭圆形透亮区,单发,好发于干骺端或长骨的中央,患骨呈对称性膨胀,密度均匀,较低。可和囊状或毛玻璃状骨纤维异常增殖症混淆。总体来讲,骨纤维异常增殖症密度较高,患骨呈不对称性膨胀,且可多发。 ;骨佩吉特病 主要侵犯骨皮质,病变范围较大,致骨皮质增厚,密度降低,骨小梁模糊,如发生在颅骨,骨纤维异常增殖症可侵犯颅底骨,本病主要是外骨板增厚,且临床表现差别更大,常发生于老年人,可有头颅增大及颅神经症状。 ;骨扫描;;;Evaluation only. Created with Aspose.Slides for .NET 3.5 Client Profile 5.2.0.0. Copyright 2004-2011 Aspose Pty Ltd.;;;在WHO(2002)新的骨肿瘤和肿瘤样病变

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