54例结节性硬化症神经系统损害临床分析_叶静.pdf

2007 8 24 4 475 : 1003-2754(2007) 04-0475-03 54 1 1 1 2 1 1 3 4 5 叶　静 , 　赵　丽, 　李存江, 　于春水, 　李丽萍 , 　王玉平, 　邹丽萍 , 　佟长顺, 　薛官英 : 54 89% ( 48/ 54) ; 84% 10 , 1 ; 63. 3% , : ; ; : 742. 89: R A The analysis neurological impairment of 54 patients with tuberous sclerosis complex YE Jing, ZHA O L i, L i - , . ( , , , Chun j iang et al B Dep artment of N eurology X uanw u H osp ital Cap ital niversity of Medical Sciences Beij ing 100053, China) Abstract: Obj ectiveT o analyze the ne rological impairment of patients w it h t bero s sclerosis com plex . Methods Fift y-fo r T SC patients w ere recr ited and their clinical data were anaylzed.T o analyze the charact ers of . - ( 48/ 54) , 84% epilepsy and mental retardant Results Eighty nine percent patients s ffered epilepsy and of the 10 ; 63. 3% . 6 epilepsy happened before years old of patients had mental handicap Kidney lesions w ere fo nd in pa- tients. ConclusionEpilepsy had a high rat io in T SC pat ients,w hich happened in the early age. Mental handicap w as common. Key words: T bero s sclerosis complex ; Epilepsy ; Mental retardant ( t bero s sclerosis complex , 1. 5 , TSC) CT M RI , 2 , 2. 1( 1) : 54 54 , 22 , 4 1%, 11 ; 32 , 59%; ( 2) : 5 , 1 11 , 9 , 9 , 3 , 2 1. 1: ; ( 3) : 1 ; 6 ; ( 4) 1998 TSC : 1 ,