後天特发性广泛无汗症-dermatol.PDFVIP

後天特發性廣泛無汗症 -四病例報告 李至偉1 蔡呈芳2 署立台北醫院皮膚科1 臺灣大學 皮膚部2 Acquired Idiopathic Generalized Anhidrosis -Four Cases Report Chih-Wei Li1 Tsen-Fang Tsai2 Acquired idiopathic generalized anhidrosis is a rare disorder. It is characterized by loss of sweating without any neurological deficit or destruction of sweat glands, and has been associated with choliner- gic urticaria. Four cases are seen in hypohidrosis special clinic (from January, 2001 to February, 2006). All the patients suffered from generalized absence of sweating and the implications of heat intolerance after exercise. Cholinergic urticaria has been associated with two cases of this acquired idiopathic gen- eralized anhidrosis. This article will discuss the clinical presentation, diagnosis and related literatures. (Dermatol Sinica 25: 226-231, 2007) Key words: Acquired idiopathic generalized anhidrosis, Eccrine gland, Cholinergic urticaria 後天特發性廣泛無汗症是一罕見疾病禿其特徵為全瘑流汗減少禿但缺少其它汗腺障礙或 神緩異常並礿膽鹼性蕁麻疹之發生相關。我們報告自90年1月至95年2月間於少汗症特別門診 所發現的四個案例。四例病例均為全瘑廣泛性流汗減少禿及運動後對熱不耐。其中兩例有蕁 麻疹之病史。本文討論後天特發性廣泛無汗症之臨床表現及診斷禿並回顧相關文獻。 ( 中華 皮誌25: 226-231, 2007) From the Department of Dermatology, Taipei Hospital, Department of Health,1 and National Taiwan University Hospital,2 Taipei Taiwan Accepted for publication: March 22, 2007 Reprint requests: Tsen-Fang Tsai, M.D., Department of Dermatology, National Taiwan University Hospital, No.7 Chung Shan South Road, Taipei 100 Taiwan TEL: 886-02FAX: 886-2 Dermatol Sinica, Sep 2007 226 李至偉 前言 汗水。病患先至小兒科診所求治禿初始診 少汗症(hypohidrosis)或無汗症(anhidro- 斷為全瘑性搔癢症禿緩數次求治無效禿乃 si