(精编)NHS临床指南 Marfan’s syndrome and related aortopathies教学课件.pptVIP

Marfan’s syndrome and related aortopathies;Marfan’s syndrome;Marfan’s syndrome and related aortopathies;Current provision of testing;Criteria : Suspected diagnosis of Marfan syndrome  REVISED GHENT CRITERIA (Loeys 2010);Feature; Score 7 indicates systemic involvement Aortic root enlargement: Z- score 2 : 20yrs Z- score 3 : 20 yrs Aortic size standardised to age and body size for accurate interpretation Z score 2.0 above 95th percentile 3.0 above 99th percentile ; Consultant Cardiologists (Adult, Paediatric) Clinic