《儿科学教学》infantilehepatitissyndrome上.ppt

Divide of gastroenterology and infectious diseases, Children’s hospital, CQMU Biliary atresia, Cholangiectasis, Caroli disease, etc metabolic abnormalities of carbohydrate ,amino-acid, protein, lipid, bilirubin, bile acid etc Hepatic primary infection hepatic involvement of general infection infection Unclear etiology and classifications Intrahepatic extrahepatic duct abnormal Etiology and Clinical manifestations Other etiologies Disorders of metabolism IHS etiology Divide of gastroenterology and infectious diseases, Children’s hospital, CQMU Malformations of the bile ducts 1. Biliary atresia 2. Congenital cholangiectasis classification： Intrahepatic extrahepatic etiology：congenital infection congenital anomaly bile ducts 3.Caroli disease 4. Alagille syndrome Etiology and Clinical manifestations Divide of gastroenterology and infectious diseases, Children’s hospital, CQMU similar clinical feature in abnormal bile duct relevance disease： pale stool，dark urine Conjunctive hyperbilirubinemia increased AKP, γ-GT level Etiology and Clinical manifestations Divide of gastroenterology and infectious diseases, Children’s hospital, CQMU 1. Biliary atresia 2. Congenital cholangiectasis classification： Intrahepatic extrahepatic etiology：congenital infection congenital anomaly bile ducts 3.Caroli disease 4. Alagille syndrome Etiology and Clinical manifestations Malformations of the bile ducts Divide of gastroenterology and infectious diseases, Children’s hospital, CQMU Caroli disease Etiology and Clinical manifestations Divide of gastroenterology and infectious diseases, Children’s hospital, CQMU 1. Biliary atresia 2. Congenital cholangiectasis classification： Intrahepatic extrahepatic etiology：congenital infection congenital anomaly bile ducts 3.Caroli disease 4. Alagille syndrome Etiology and Clinical manifestations Malfor