先天性长QT综合征的诊治进展特点和管理.pdfVIP

先天性长QT综合征的诊治进展特点和管理 滕腾;黄美容 【摘要】Congenital long QT syndrome(LQTS) is a latent lethal cardiac channelopathy disease,most commonly seen in children and puberty.At the onset of the disease,some patients present with de pointes ventricular tachycardia,syncope and sudden death as the first clinical symptoms,and most of them may have no obvious clinical symptoms.The diagnosis mainly includes family history,clinical features and electrocardiograph,while currently gene test is another essential methoed,obviously increasing the positive diagnosis rate.Management of patients with