Ebstein畸形的外科治疗.pptxVIP

Ebstein畸形的外科治疗第1页/共51页 Ebstein畸形是罕见复杂的心脏先天畸形发生率1:40,000-200,000先天性心脏病中: 1%疾病谱宽： 轻型 无症状 重症 新生儿期死亡率极高 手术死亡率高Wilhelm Ebstein 1866 年首先描述形态Helen Taussig 1950 年描述临床特点第2页/共51页 解剖学特点Displacement of the septal and posterior leaflets of the TV toward the apex of the RV.Although the anterior leaflet is attached at the appropriate level of the tricuspid annulus, it is larger than normal and may have multiple chordal attachments to the ventricular wall.第3页/共51页 3. The segment of the RV from the level of the true tri