弥漫性肺间质性疾病.pptxVIP

弥漫性肺间质性疾病;弥漫性肺间质性疾病（inter;肺间质的概念肺实质―指肺各;肺间质指肺泡间及终末气道上皮;无标题;解剖学上肺间质①脉管周围的间;细胞成份：75%是细胞成份。;肺间质性疾病的发病机理ILD;分型按肺泡内炎症和免疫效应细;病理过程--肺泡炎期肺泡间膈水;肺泡炎期;炎性介质及胶原酶和弹性蛋白酶破;肺损伤期;病理过程--修复及纤维化期肺间;Thenormalwoun;schemeofthea;肺水肿;修复及肺间质纤维化期;无标题;无标题;病理过程--胶原代谢异常早期;Contrastingpat;ILD类疾病1.根据发病缓急;病因分类病因已明吸入无机粉尘：;病理分类⑴、肉芽肿性肺间质性;Langerhanscell;Lymphangioleiom;Emphysema;systemicsclero;systemicsclero;Pneumocystisca;FollicularBron;Follicularbron;无标题;无标题;Follicularbron;结节病大体标本;结节病;特发性间质性肺炎（IIPS）分;特发性间质性肺炎（IIPS）分;Diffuseparench;ATS/ERS最新临床-影像-;特发性间质性肺炎的病理特点行;UIP、NSIP、DIP、AI;ILD临床表现症状进行性加重性;实验室检查胸部影像学检查①胸;无标题;无标题;肺功能：限制性通气功能障碍为主;histologicdiag;CTFindingUIP9;间质性肺炎临床及病理特点1.;Idiopathicpulm;Idiopathicpulm;Usualinterstit;UIP;UIP;UIP;Idiopathicpulm;Idiopathicpulm;2.脱屑性间质性肺炎（DIP）;Desquamativein;Desquamativein;Desquamativein;Desquamativein;DIP;DIP;Desquamativein;Desquamativein;3.呼吸性细支气管炎间质性肺病;Respiratorybro;Respiratorybro;Respiratorybro;4.急性间质性肺炎（AIP）属;acuteinterstit;acuteinterstit;acuteinterstit;acuteinterstit;Acuteinterstit;acuteinterstit;Acuteinterstit;Acuteinterstit;acuteinterstit;AIP;AIP;acuteinterstit;非特异性间质性肺炎（NSIP）;Nonspecificint;Nonspecificint;Nonspecificint;Nonspecificint;NSIP;NSlP;NSIP.;Nonspecificint;Nonspecificint;cryptogenicorg;闭塞性细支气管伴机化性肺炎⑴起;cryptogenicorg;cryptogenicorg;cryptogenicorg;cryptogenicorg;cryptogenicorg;2.淋巴细胞性间质性肺炎（LI;lymphocyticint;Lymphoidinters;Lymphoidinters;Lymphocyticint;Lymphoidinters;Lymphoidinters;3.巨细胞性间质性肺炎（GIP;亦称为隐原性纤维化性肺泡炎是一;诊断标准：①肺活检诊断为UIP;治疗①常规强的松05mg/kg;弥漫性泛细支气管炎（DPB）;DPB;DPB;谢谢