羊膜带综合征相关畸形与相关因素, 诊断及处理结果分析.docVIP

羊膜带综合征相关畸形相关因素及处理结果分析） 【Author brief introduction】Liang Li ( 1973-5 ), female, Bachelor of medicine, attending physicians. E-mail: 315792402@, mobile phoneresearch directions: prenatal diagnosis。 摘要：目的报告例羊膜带综合征(ABS),对其伴有的复杂畸形进行探讨羊膜带综合征相关畸形的相关因素及处理结果方法:对例ABS进行羊膜粘连带及受累组织进行组织学观察结果:本为严重的不对称的复合性畸形,包括头面部、腹壁及肢体等异常, 病例找到明确的羊膜带粘连证据粘连带为纤维结缔组织 ,可见羊膜上皮皮肤或头皮-羊膜粘连处为羊膜的中胚层面粘合于表皮下的结缔组织,腹壁缺损缘为羊膜逐渐向皮肤鳞状上皮移行(羊膜-外胚层过渡带)结论:ABS主要表现为外表面组织器官缺陷;受累组织器官由于其在发生的关键时期,因羊膜囊破裂及羊膜带粘连受到干扰而致畸;畸形的严重程度及范围取决于羊膜囊破裂的时间和部位Abstract】 Objective to report 2 cases of amniotic band syndrome ( ABS ), its associated with malformation complex analysis, explore the amniotic band syndrome associated malformations associated factors, diagnosis and treatment result analysis. Methods: 2 cases of ABS B ultrasound image analysis of results, which a case of amniotic adhesion bands and the involved tissues for histological observation. Results: in the 1 cases of serious asymmetric composite deformities, including the head and face, abdominal and limb abnormalities, the case can be found clear evidence of amniotic band adhesion, adhesion with fibrous connective tissue, visible amniotic epithelial, skin or scalp - amniotic adhesions as amniotic mesoderm surface bonded to the epidermis under connective tissues, abdominal wall defect edge for amniotic membrane gradually to cutaneous squamous epithelial migration ( amniotic - ectoderm transition zone ). Another example is a simple meningoencephalocele malformations, all cases of B ultrasound imaging in amniotic fluid can be seen floating band echo, the part attached to the fetus; amniotic band adhesions of fetal limb portion of visible deformity deformity, often to scan the amniotic band echo the adhesion. Conclusion: ABS mainly for outer surface of tissue and organ defects; involvement of tissue and organ because of its occurrence in the critical period, because of the amniotic sac and amniotic membrane rupture with adhesions interference and teratogenicity; the s