Mondini内耳畸形的诊断与治疗.pdfVIP

8 Chin J Otor hinolaryngol, Febr uary 1997, Vol 32, No. 1 M ondini 杨伟炎　方耀云　杨仕明　韩东一　黄德亮　石勇兵　吴　涛 , 5( 6) Mondini 4( 5) ( 3Klippel-Feil ) , 1 : ¹ , ; º CT M on- dini , ; » , , , Diagnosis and management of Mondini malform ationYang W eiy an , Fang Yaoy un , Yang Sh im ing , et al . Ch inese PL A General H osp ital , B e ij ing 100853 Abstract Owing to t he de elopment of imaging technology and audiology, some of the sen- sorineural hearing loss cases that were pre icusly considered t o be of unknow n cause ha e been found to be inner ear malformation. Fi e cases of Mondini malformat ion are re iew ed in this paper . CSF o- , - , torhinorrhea occurred in four cases Klippel Feil syndrome in three and concurrent otosclerosis in . , : 1) one patient In discussion the authors point out t hat CT scanning is an supplement to audiologic tests for such patients; 2) perilymph fistula in Mondini malformation is oft en found at the o al w in- dow and its icinit y, the foot plat e and the round w indow ; 3) the fistula can be treated by plugging . w ith fascial t issue ia tympanoplast ic approach w it h endaural incision The mucosa around the fist ula should be st ripped away and the plugging tissue should be of dum b-bell shape. Key words LabyrinthAbnormalitiesCerebrospinal rhinorrhea Cerebrospinal ot orrhea , M ondini 5( 6) , , , 3, 2; 4, 5 11 , , , M ondini ,