CTandMRImagingoftheInnerEarandBraininChildrenwithCongenitalSensorineuralHearingLoss重点分析.pptVIP

CT and MR Imaging of the Inner Ear and Brain in Children with Congenital Sensorineural Hearing Loss 先天性感音神经性聋患儿内耳及脑部CT、MRI表现  PART Ⅱ第二部分 Complete Labyrinthine Aplasia 迷路未发育 Complete labyrinthine aplasia, also known as Michel aplasia (because it was first described by Michel in 1863), is the most severe form of inner ear deformity; it is caused by developmental arrest of the otic placode during the 3rd gestational week 迷路未发育又称为米歇尔畸形（Michel畸形），1863年由米歇尔首次提出，是最严重的内耳畸形，是由于妊娠第3周听基板发育停止引起的 The condition is extremely rare, accounting for only 1% of all inner ear malformations 这种畸形非常少见，占全