DIAGNOSIS, TREATMENT, RADIOLOGIC AND PATHOLOGIC FINDINGS OF SPLENIC ANGIOSARCOMA; A CASE REPORT.docVIP

CASE REPORT DIAGNOSIS, TREATMENT, RADIOLOGIC AND PATHOLOGIC FINDINGS OF SPLENIC ANGIOSARCOMA: A CASE REPORT ?zgür Ekinci , ?zlem Okur , Fikret Aksoy , G?khan Demiral , Taner Evcimik , Haydar Yalman1, 1 1 2 2 1 Rafet Yi?itba??1 1 Sa?l?k Bakanl??? G?ztepe E?itim Ara?t?rma Hastanesi, 3. Genel Cerrahi Klini?i, ?stanbul, Türkiye Sa?l?k 2 Bakanl??? G?ztepe E?itim Ara?t?rma Hastanesi, 2. Genel Cerrahi Klini?i, ?stanbul, Türkiye ABSTRACT Although primary splenic angiosarcomas are the most common malignant nonhematopoietic tumors of the spleen ,they are extremely rare tumors with very poor prognosis. These tumors are highly aggressive and lethal, present with widespread metastasis or splenic rupture. Definitive diagnosis and treatment is surgical and survival is significantly improved when splenectomy is performed prior to rupture. Diagnosis, radiologic and pathologic findings and treatment of a patient with primary splenic angiosarcoma are presented. Keywords: Angiosarcoma, Spleen, Immunohistochemistry, Imaging SPLEN?K ANJ?OSARKOMANIN TANISI, TEDAV?S?, RADYOLOJ?K VE PATOLOJ?K BULGULARI:OLGU SUNUMU ?ZET Primer splenik anjiosarkomalar dala??n hematopoetik sistemle ili?kili olmayan en s?k malign tüm?rleri olmas?na kar??n olduk?a nadir g?rülmekte ve prognozu son derece k?tüdür. Bu tüm?rlerin seyri olduk?a agresif ve ?lümcül olup yayg?n metastazlar veya dalak rüptürü ile kar??m?za ??karlar. Kesin tan? ve tedavi cerrahi ile olur ve rüptür ?ncesi uygulanan splenektomi ya?am süresini anlaml? ?ekilde uzat?r. Primer splenik anjiosarkomal? bir hastan?n tan?, radyolojik patolojik bulgular ve tedavisini sunuyoruz. Anahtar Kelimeler: Anjiosarkoma, Dalak, ?mmünhistokimya, G?rüntüleme INTRODUCTION Primary malignant splenic mesenchymal tumors are extremely rare . These tumors, the CASE REPORT 1 A 50 year-old male patient was admitted with left upper quadrant pain, fatigue and weight loss of 7 kg in 2