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of Vitamin D Deficiency维生素D缺乏性佝偻病课件
Definition Rickets, a deformative disease that occurs among children, are characterized by deficient mineralization of the bone matrix(骨基质) as a result of deficiencies of calcium or phosphorus or both. Defective mineralization at the growth plate Osteomalacia(骨软化) at the corticoendosteal level Source and Metabolism of Vitamin D Animal food: Vit D3 Vegetal food: Vit D2 ergosterin(麦角固醇) ergocalciferol(麦角骨化醇) Etiology less outdoor activity high buildings pollution season Etiology VitD3 calcium Etiology premature low- birth weight twins infants adolescents Etiology Clinical manifestation Clinical manifestation Clinical manifestation Clinical manifestation Clinical manifestation Clinical manifestation Clinical manifestation Clinical manifestation Clinical manifestation Symptoms and signs ? 不规则钙化线,钙化带致密增宽、骨质密度 逐渐恢复 Clinical manifestation Diagnosis History Clinical manifestation Serum calcium level (±) Serum phosphorus level↓ Serum alkaline phosphatase level↑ 25(OH)D38ng/ml Treatment Natural sunlight Oral administration of VitD VitD 2000-6000 IU/d ×2-4w? 400IU/d Impulsive injection of VitD VitD 30-60万IU 2-3 times ? 400IU/d Calcium 0.5-1.0g/d Othopedics Prevention Nutrition Exposure to sunlight Oral administration of VitD 400IU/d (2w-2y) Double for LBW, premature and twins EP: VitD 500-1000Iu/d Differentiate diagnosis 男,12岁,因身材矮小、行走乏力而就诊 3岁前生长基本正常 家族中有类似患者 曾给予VitD治疗,无效;后服用罗钙全(活性VitD),并同时补充磷制剂 身高132cm 血钙正常,血磷明显降低,25(OH)D3正常 X线杯口状比去年更严重 Summary Pathology Clinical manifestation Diagnosis Treatment and prevention Reference 维生素D缺乏性佝偻病防治建议。 中华儿科杂志2008,46(3):190-191 Prevention of rickets and vitamin D deficiency in infants, children, and adolescents. Pediatrics 2008; 122:1142-1152 儿童低磷抗维生素D佝偻病23例。临床荟萃2008,23(3):205-206 维生素D缺
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