肺动脉高压流行病学和我国PAH资料分析.pptVIP

In 1891, the German pathologist Romberg observed that the heart of an individual, suffering from a stricture of the pulmonary arteries due to severe sclerosis, was double the size of a man′s fist. He again named this disease sclerosis of the pulmonary arteries. 当前1页，共25页，星期日。 1. 肺动脉高压 特发性肺动脉高压 遗传性 BMPR2 ALK1, endoglin 未知突变 药物或毒物 相关性 结缔组织病 心脏或大血管左向右分流 门脉高压 HIV 感染 血吸虫病 慢性溶血性贫血 1′肺静脉闭塞病，肺毛细血管瘤样病 2. 左心疾病相关肺高血压 收缩功能障碍 舒张功能障碍 瓣膜病 COPD 间质