Marfan syndrome lens subluxation lens the hands of France injection suction treatment.doc

 PAGE \* MERGEFORMAT 6 Marfan syndrome lens subluxation lens the hands of France injection suction treatment Keywords:: Marfan syndrome Marfan syndrome is a congenital ectodermal dysplasia disease, bone, cardiovascular and eye involvement of its features. Eye lesions more vulnerable because of lens suspensory ligament, causing the lens up or subluxation of the nose, seriously affecting vision need to surgical treatment, surgical methods of selection and operation must be in accordance eye surgery to determine the specific condition. I reported one cases of Marfan syndrome, lens subluxation in patients with severe hands and Law Enforcement lens injection-aspiration successful treatment of cases is as follows. A clinical data 1.1 General information on patients, male, 17 years old. With binocular visual impairment on July 5, 2005 come to my hospital treatment. Check visual acuity right eye 0.08, left eye 0.06, are not correct. Intraocular pressure: the right eye 17.5mmHg, left eye 18mmHg. Eyes, conjunctival no hyperemia, corneal transparency, slightly lower anterior chamber depth, iris micro-tremors, pupil round, diameter 3mm, light response from the slow upward subluxation of the lens, the pupil is not easy, scattered large, post-dilation can be seen below the suspensory ligament of the lens. Fundus optic disc vertical oval, there are temporal arc spot, leopard-like fundus, retinal blood vessels without exception. Ultrasound axial length measurement: the right eye 25.25mm, left eye 25.50mm. The patient’s body slender (height 175cm, weight 61kg), the lack of subcutaneous fat, muscle tone flaccid, loose joints, limbs and hand-foot-long and thin, spider-like fingers (toes), echocardiography shows widened aortic diameter, mitral valve before and after the leaf prolapse, in line with Marfan syndrome, but no family history. 1.2 Treatment of cases of lens subluxation due to the heavier, more difficult to extend pupil also not suitable for doing capsular tension ri