风湿性疾病相关综合征课件.pptx

风湿性疾病相关综合征的诊治龙现明A summary of syndromes (1)Felty syndromeReiter’s Syndrome (Reactive Arthritis) PONCET syndromeCREST syndromeChurg-Strauss syndromeHemophagocytic syndromeMacrophage Activation Syndrome SAPHO syndromeParaneoplastic rheumatologic syndromePOEMS syndromeEhlers-Danlos syndromeWeber-Christian syndromeA summary of syndromes (2)Caplan’s syndromePalindromic syndrome Shrinking lung syndromeThrombotic thrombocytopenic purpura–hemolytic uremic syndrome (TTP-HUS) Neuropsychiatric lupus (NPSLE) syndromeLambert-Eaton myasthenic syndrome (LEMS)Sweet’s syndrome Chronic Infantile Neurologic Cutaneous and Articular (CINCA) SyndromeParry-Romberg syndromeSjogren’s syndromeAntiphospholipid syndrome (APS)Bechet’s syndromeRS3PE syndromeOverlap syndromeRaynaud’s syndrome Undifferentiated polyarthritis syndromeLupus anticoagulant hypoprothrombinemia syndrome (LAHS)Rowell’s syndromeDrug-induced lupus syndromesCogan’s syndromeLarge granular lymphocyte syndrome Other syndromesStiff skin syndromeWerner’s syndrome Shulman’s syndrome or fasciitis-panniculitis syndromeCarcinoid syndromeEosinophilia-myalgia syndromeChronic fatigue syndrome Toxic oil syndromeParry-Romberg syndrome Hypocomplementemic urticarial vasculitis syndromeHypereosinophilic syndrome Papular-purpuric gloves and socks syndrome (PPGSS)L?fgren’s syndromeHemolytic uremic syndrome HELLP (hemolysis, elevated liver enzymes, low platelets) syndrome Waterhouse-Friderichsen syndrome (WFS)Carpal tunnel syndrome Milwaukee shoulder syndrome Greater trochanteric pain syndromeFemoroacetabular impingement syndromeDemyelinating syndromesFrank nephrotic syndrome Cold agglutinin syndrome Hyperviscosity syndromeFelty’s syndromeFelty’s syndrome (FS)：定义1924年由A.R Felty首先提出，用于描述慢性关节炎、脾大、粒细胞减少三联征见于血清阳性侵蚀性强的RA，为RA患者罕见的症状群，在美国RA患者中发生的概率约为1-3%RA患者出现FS提示关节炎及关节外表现严重、预后差Felty’s syndrome (FS)：诊断关节外表现：类风湿结节（76%）体重下降（68%）干燥综合征（56%）淋巴结肿大（34%）下肢溃疡（25%）胸膜炎（19%）皮肤色素沉着（17%）周围神经病变（17%）巩膜炎（8%）三联征：Rheumatoid arthritis (RA)Neutropenia (中性粒细胞减少)Splenomeg