白塞病的诊断和治疗精要.ppt

概述 多系统、多器官受累的自身免疫性疾病 丝绸之路病（多见于日本、中东及地中海盆地一带）。 属于系统性血管炎的一种 扑朔迷离 可累及静脉和动脉 临床最具特征的三联症 口 眼 外阴生殖器 The Chapel Hill Consensus Conference (1994) Large vessel vasculitis Giant cell (temporal) arteritis (GCA) Takayasu arteritis Medium-sized vessel vasculitis Polyarteritis nodosa (PAN) Kawasaki disease Small vessel vasculitis Wegeners granulomatosis (WG) Churg-Strauss syndrome (CSS) Microscopic polyangiitis (MPA) Henoch-Schoenlein purpura (HSP) Essential cryoglobulinemic vasculitis (ECV) Cutaneous leukocytoclastic vasculitis (CLV) Possible thrombophlebitis, or superficial venous thrombo