前期报告两侧右心房症病儿之猝死与心不整脉之关联中文摘要两.PDFVIP

前期報告 ：兩側右心房症病兒之猝死與心 noncardiac in 5 (23%)(fulminant sepsis with 不整脈之關聯 positive blood culture: streptococcus 一 、中文摘要 pneumonia 3, E. coli 1 and yeast-like organism 1). Freedom from sudden death 兩側右心房症之病兒不但常合併有複 steadily decreased with age until the age of 3 雜先天性心臟病 ，例如肺靜脈回流異常、 years. 單一心房 、心內膜墊缺損、單一心室及肺 Conclusions. The incidence of sudden death in RAI patients after initial palliation 動脈狹窄等 ，導致新生兒期之發紺或心衰 was still very high. The sudden death was 竭 ，同時也常合併心臟傳導系統異常，如 related to the complex cardiac anomalies per 多重房室結及竇房結 。這些傳導系統之異 se, a susceptibility to fulminant infection, and 常經常導致上心室頻脈 。至於這些不整脈 arrhythmia. 的發生是否會影響這些病兒之預後 ，目前 Keywords: Sudden death, complex congenta 仍不清楚。本研究以20年之病兒長期追蹤 heart disease, conduction system 為研究對象 ，發現即使在接受心臟之輔助 anomalies 手術治療 ，這些病兒極高的概率發生猝 死 ，這些猝死只有9%與心律不整有關。最 二 、緣由與目的 重要的仍是心肺功能不足(68)% ，猛暴性感 染(23)% 。 It has been estimated that about 40% of 關鍵詞 ：心律不整、複雜先天心臟病、傳 sudden cardiac death in pediatric patients 導系統異常 occurs in the patients with unoperated congenital heart disease or acquired heart 1 Abstract disease. Congenital heart disease with Sudden death in patients with right atrial abnormal conduction system, e.g., corrected isomerism after palliation transposition of great arteries and Ebstei