8 cases of male pseudohermaphroditism diagnosis and treatment.docVIP

 PAGE \* MERGEFORMAT 13 8 cases of male pseudohermaphroditism diagnosis and treatment [Abstract] Objective To investigate the diagnosis and treatment of male pseudohermaphroditism. Methods of diagnosis and treatment of the past 15 years, 8 cases of male pseudohermaphroditism patients with information and literature to analyze their causes, diagnosis and treatment were discussed. Results 8 patients underwent surgery to maintain female sex, oral estrogen replacement therapy after surgery, were followed up 1 to 15 years, 6 cases of prepubertal physical development normal, all patients satisfied with the appearance of external genitalia, feel good, and 2 cases of secondary sexual characteristics after 2 years of improvement, 1 Married, sex life is normal. Conclusion of postoperative male pseudohermaphroditism female gender choice is appropriate, but early diagnosis and treatment on quality of life and quality of life of patients is important. [Keywords:] diagnosis and treatment of pseudohermaphroditism Gender male pseudohermaphroditism is a type of phenotypic abnormalities, the patient gonad to testes, but outside the reproductive tract and lack of normal male genital development, which appears to some extent, female phenotype. From 1994 to 2008 were treated in the author 8 cases, are as follows. 1 Materials and Methods The 8 patients were female gender, karyotype were 46, XY, aged 7 to 20 years, mean 12 years, including 7 cases of abnormalities or the appearance of external genitalia showed bilateral groin or labia majora tumor and treatment , 1 case found that the appearance of abnormal external genitalia and lower abdominal mass were more than 1 year of treatment increased. All the patients body, skin, subcutaneous fat, showed a feminine voice, no Adam’s apple, no beard, no breast development, the appearance of the external genitalia female-dominated, the size of the labia, have a length of 1.5 ~ 3.5 cm of the blind-side the vagina, clitoris is