Glycogen accumulation of Nursing of patients.docVIP

 PAGE \* MERGEFORMAT 11 Glycogen accumulation of Nursing of patients [Abstract] Objective 4 cases of the disease glycogen disease observed cumulative sum up nursing experience. Methods 2001-2009 4 patients were treated in our department glycogen accumulation disorder in children is reviewed and summarized. Results 4 patients suffering from After the children were discharged in stable condition in hospital without any complications during the period. Conclusions treatment follow doctor’s orders to strengthen the clinical observation and nursing care can reduce complications, reduce the children’s physical and mental suffering and improve the prognosis in children. [Keywords:] glycogen accumulation of disease, care Glycogen accumulation disorder (hepato glycogenosis, also known as glycogen storage disease type or Von Gierke disease, is difficult to cure a rare congenital metabolic diseases, is a kind of congenital defects in the enzymes of glycogen metabolism disease, the incidence rate of 1 / 50000 ~ 100000 [1]. mainly due to liver and kidney glucose -6 phosphate enzyme deficiency caused by autosomal recessive disease [2]. clinically to repeated hypoglycemia, lactic acidosis with hepatomegaly, hepatic steatosis and hyperlipidemia characterized. children with growth retardation, susceptibility may be due to severe acidosis, gout, nephritis caused by renal failure and death. Therefore, strengthening disease surveillance, control low blood sugar, keep blood sugar steady progress in the prevention of infection to control the disease focus of nursing. our department since 2001, children were treated 4 cases of the disease, now nursing reported as follows. 1 Clinical data The group of 2 females, 2 males, all aged 9 months to 1 year, 2 years 3 months, 4 years, 8 years old, admitted to hospital complained of fatigue, anorexia, diarrhea in 1 case, 1 case of abnormal liver function, liver function abnormalities, abdominal distension, and progressive weight