Progeria care of 1 patient with heart failure.doc

 PAGE \* MERGEFORMAT 7 Progeria care of 1 patient with heart failure [Keywords:] progeria; heart failure; Care Progeria (progeria) is a rare metabolic disorders, developmental disorders and the dwarf state, accompanied by bones, teeth, nails means, such as hypoplasia of hair and fat to look and atherosclerosis childhood for the performance characteristics of the elderly. The disease was first , respectively, by the Hutchinson and Gilford in 1886 and 1904 reports, also known as Hutchinson-Gilford progeria syndrome [1]. both men and women sick. its incidence is about 1 / 800 million. our department admitted in February 2009 1 cases of progeria patients with heart failure, the active treatment and care, patient improved and discharged, now nursing reported as follows. A case report Patients, male, 38 years old, due to repeated chest tightness, suffocation 2 years, 15 days increased with the admission can not be supine. Examination: Pulse 90 times / min, breathing 26 times / min, blood pressure 17.29/9.31kPa, height 160cm, weight 30kg, poor growth, malnutrition. responsive, dentition abnormalities, sounds vague. loose wrinkled skin, subcutaneous fat, meager. head of a larger, full-bald forehead protrusion, facial wrinkles more than cheek slim the nose prominent. thorax small, barrel chest, lungs breath sounds rough, the end could be heard and a small amount of lung auscultation. heart rate 120 beats / min, regular law, precordial auscultation area and aortic valve could be heard and 3 / 6 systolic murmur. enlargement of the liver, ribs 5cm, tender. slender limbs, small limbs, lower limbs edema. biceps, triceps hyperreflexia. echocardiography showed: aortic valve, two severe stenosis and mitral regurgitation, severe pulmonary hypertension, pericardial effusion. electrocardiogram analysis showed: sinus tachycardia, left atrial big. B-show: the left kidney with multiple stones, large bilateral pleural effusion, a small amount of ascites. past pneumonia, ki