鼻侧腱膜固定法在先天性小眼症内眦赘皮矫正中应用.docVIP

鼻侧腱膜固定法在先天性小眼症内眦赘皮矫正中应用[摘要]目的:探讨鼻侧腱膜固定法在先天性小眼症内眦赘皮矫正中的临床应用效果。方法:2007年1月至2009年1月,采用鼻侧腱膜固定法矫正内眦赘皮联合上睑下垂矫正术,矫治先天性小眼症16例。16例均行鼻侧腱膜固定法矫正内眦赘皮,以及上睑提肌悬吊术或额肌悬吊术矫正上睑下垂,其中5例联合行外眦开大成形术。结果:术后内眦赘皮消失,睑裂横径、纵径和内眦间距增大,重睑线自然美观。术后获随访3月～2年 ,效果良好。结论:进行鼻侧腱膜固定法矫正先天性小眼症中的反向内眦赘皮,术后瘢痕少恢复好,效果确切。 [关键词]先天性小眼症;内眦赘皮;鼻侧腱膜固定法. [中图分类号]R622[文献标识码]A[文章编号]1008-6455(2010)01-0037-03 Fixation of latefal nasal aponeurosis :the aplication of epicanthus correction in the congenitalblepharophimosissyndrome FU Si-qi,SONG Jian-xing,CHEN Jiang-ping,ZHAO Lin (Department of Plastic Surgery,Changhai Hospital,Second MilitaryMedical University,Shanghai 200433,China) Abstract: ObjectiveTo explore the clinical effect of aplicating fixation of latefal nasal aponeurosis to correctepicanthus for congenital blepharophimosis syndrome. Methods From January 2007 to January 2009,16 patients (32 sides) with congenital blepharophimosis syndrome were treated.16 patients underwent medial canthoplasty with fixation of latefal nasal aponeurosis and blepharoptosis correction with frontalis suspension or suspension of levator palpebrae superioris,and 5 patients were also given lateral canthoplasty at one-stage. ResultsThe post operative transverse dimension and vertical dimension of the palpebral tissue and the inter canthal distance became lager.The supratarsal fold in the upperlid was natural. With a follow up of 3 months to 2 years,all patients were satisfied with their results. ConclusionAplicating fixation of latefal nasal aponeurosis to correct epicanthus for congenital blepharophimosis syndrome can achieve good result for blepharophimosis syndrome with lesser tissue damage,faster recovery and more favorable postoperative formation. Key words:congenital blepharophimosis syndrome;epicanthus;fixation of latefal nasal aponeurosis 先天性小眼症,又称Komoto综合征、先天性睑四联征、小睑裂综合征、小眼裂畸形,世界上由Galezow ski 首先报道, Komoto于1912年详细描述[1]。它是一种常染色体显性遗传病,临床表现为先天性睑裂狭窄、逆向性内眦赘皮、上睑下垂和内眦远距,部分患者伴鼻梁低平、下睑外翻、上眶缘发育不良、眉毛密集粗黑等。传统治疗先天性小眼症中的反向内眦赘皮方法大多使用